Portal Hypertension Complicating Choledochal Cyst

In the literature, CC presenting with PH has not been addressed adequately and there is a paucity of literature on CC complicated by PH. Gastrointestinal bleeding, splenomegaly or incidental discovery of esophageal varices led to the diagnosis of associated PH. Excision of CC and bilio-enteric bypass may not be feasible in those patients as there is a formation of massive collaterals in the region of porta associated with secondary PH. [5,6] An initial approach of internal drainage (endoscopic/ operative) of the cyst may allow regression of collaterals and subsequent safe excision of the cyst in this difficult group of patients.